X-linked hypohidrotic ectodermal dysplasia management with removable prosthesis in a pediatric patient. Case Report
نویسندگان
چکیده
Introduction: Ectodermal dysplasia is a rare genetic disorder that affects structures derived from ectoderm such as teeth, hair, nails, and sweat glands. Oligodontia common finding the chewing, smiling self- esteem of these pediatric patients. Case Report: We present case report 7-years-old patient who consulted with his mother, showing same condition. The intervention consisted removable prosthesis satisfactory results. Conclusion: X-linked hypohidrotic ectodermal represents challenge for dentist offers rehabilitation to according craniofacial development, age, socioeconomic status, number missing teeth.
منابع مشابه
Treatment with removable prosthesis in hypohidrotic ectodermal dysplasia. A clinical case.
Ectodermal dysplasias form part of a wide range of syndromes presenting abnormal development of two or more tissues derived from the ectoderm. Hypohidrotic ectodermal dysplasia is a congenital syndrome, characterized by hypotrichosis (hair is sparse, fine and weak; anomalies in the skin and nails), hypohidrosis (due to the paucity of sweat glands which in turn gives rise to sweat disorders) and...
متن کاملHypohidrotic ectodermal dysplasia--a case report.
A case presented here is that of a nine year old male patient with total anodontia. Findings of this case as regards to the orofacial, radiographic and other general manifestations were suggestive of hypohidrotic ectodermal dysplasia. The dental problems were best managed by prosthetic replacement of dentition taking into consideration a design which would provide adequate relief for the preser...
متن کاملComplete and Removable Partial Prosthesis for a Child with Hypohidrotic Ectodermal Dysplasia
Young children with hypodontia caused by hypohidrotic ectodermal dysplasia (HED) not only have difficulties in mastication and speech but can also sense that their appearance is different from others. Enabling children with HED to look like their peers through the use of well-fitting and functioning complete and removable partial dentures with age appropriate teeth will greatly assist in their ...
متن کاملPossible genetic heterogeneity in X linked hypohidrotic ectodermal dysplasia.
Hypohidrotic ectodermal dysplasia has been mapped to Xq11-q13 by linkage studies and by a translocation in a manifesting female. We report a family with hypohidrotic ectodermal dysplasia in which the disease did not segregate with this region of the X chromosome as expected. Ten DNA probes which are localised between Xp11 and Xq22 were used in the investigation. The difficulties in diagnosing t...
متن کاملLung and eye involvement in X-linked hypohidrotic ectodermal dysplasia
Objective X-linked hypohidrotic ectodermal dysplasia (XLHED; ectodysplasin deficiency) has been classically described as affecting hair, sweat glands and dentition. What may be underappreciated is the effect ectodysplasin deficiency has on glands surrounding the airways and eyes and the resulting chronic health issues. In this study, we evaluated respiratory and ocular symptoms in XLHED patients.
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ژورنال
عنوان ژورنال: Journal of Oral Research
سال: 2022
ISSN: ['0719-2479', '0719-2460']
DOI: https://doi.org/10.17126/joralres.2022.055